Alacam, AlevGuclu, Zeynep AsliHasanoglu, Alev2024-06-122024-06-1220152147-9445https://doi.org/10.4274/jpr.85856https://hdl.handle.net/20.500.14551/21716Hypodontia is defined as the congenital missing of one or more teeth in one or both dentition periods. In this case report, ketone utilization disorder with oro-dental findings was reported which was previously not reported in the literature. It was concluded that dental examination is an important parameter which must be taken into consideration in the future case reports.en10.4274/jpr.85856info:eu-repo/semantics/openAccessHypodontiaKetone Utilization DisorderCongenitalKetone Utilization Disorder and HypodontiaArticle2299101N/AWOS:000219056100011