Celik S.Yazici Y.Sut N.Yazici H.2024-06-122024-06-1220150392-856Xhttps://hdl.handle.net/20.500.14551/17716Objective. To investigate the frequency of Behçet's syndrome (BS) with pulmonary artery aneurysms (PAA) publications, the most lethal complication of BS, as reported from different countries and to provide a review of diagnostic techniques, treatment approaches and prognosis. Methods. Countries from each continent with a population of 4 million and over were chosen (n=128). A PubMed search for "BS, PAA and the country name" was conducted and 23 countries with BS and PAA were identified. The full texts of articles (n=91) were analysed for data including gender, age, accompanying vascular findings, diagnostic techniques, treatment modalities and mortality rates. Results. A total of 207 (183 males, 24 females) patients with BS and PAA were reported in 91 articles originating from 23 countries. As expected there was a significant correlation (r=0.88, p < 0.001) between the total number of articles about BS (n=4431) and those related to PAA and BS. In a simple linear regression analysis the number of BS and PAA articles from Japan was significantly below the identity line while in Turkey there was a propensity to publish more articles related to PAA than expected. One hundred and sixteen patients (56%) were treated with immunosuppressive therapy. Biologics were used only in 5 patients (2%). Of the 207 patients, 62 (30%) died. Conclusion. PAA is mostly reported as case reports from countries where BS is common. PAA might be uncommon in Japan. The prognosis of PAA could be getting better. © Clinical and Experimental Rheumatology 2015.eninfo:eu-repo/semantics/closedAccessBehçet's Syndrome; Pulmonary Artery AneurysmsBiological Product; Immunosuppressive Agent; Africa; Age; Artery Surgery; Article; Artificial Embolism; Asia; Behcet Disease; Diagnostic Procedure; Europe; Gender; Geography; Human; Immunosuppressive Treatment; Japan; Medical Literature; Mortality; Mortality Rate; North America; Pacific Islands; Priority Journal; Prognosis; Publication; Pulmonary Artery Aneurysm; South America; Turkey (Republic); Adolescent; Adult; Aneurysm; Behcet Syndrome; Female; Male; Middle Aged; Pulmonary Artery; Risk Factor; Young Adult; Adolescent; Adult; Aneurysm; Behcet Syndrome; Female; Humans; Male; Middle Aged; Prognosis; Pulmonary Artery; Risk Factors; Young AdultArticle3354592-s2.0-8495458281826211653Q2