Celik, S.Yazici, Y.Sut, N.Yazici, H.2024-06-122024-06-1220150392-856Xhttps://hdl.handle.net/20.500.14551/19018Objective. To investigate the frequency of Behcet's syndrome (BS) with pulmonary artery aneurysms (FAA) publications, the most lethal complication of BS, as reported from different countries and to provide a review of diagnostic techniques, treatment approaches and prognosis. Methods. Countries from each continent with a population of 4 million and over were chosen (n=128). A PubMed search for BS, FAA and the country name was conducted and 23 countries with BS and FAA were identified. The, full, texts of articles (n=91) were analysed for data including gender, age, accompanying Vascular findings, diagnostic techniques, treatment modalities and mortality rates. Results. A total of 207 (183 males, 24 females) patients with BS and FAA were reported in 91 articles originating from 23 countries. As expected there was a significant correlation (r=0.88, p<0.001) between the total number of articles about BS (n=4431) and those related to FAA and BS. In a simple linear regression analysis the number of BS and FAA articles from Japan was significantly below the identity line while in Turkey there was a propensity to publish more articles related to FAA than expected. One hundred and sixteen patients (56%) were treated with immunosuppressive therapy. Biologics were used only in 5 patients (2%). Of the 207 patients, 62 (30%) died. Conclusion. FAA is mostly reported as case reports from countries where BS is common. FAA might be uncommon in Japan. The prognosis of FAA could be getting better.eninfo:eu-repo/semantics/closedAccessBehcet's SyndromePulmonary Artery AneurysmsVascular InvolvementDiseaseManifestationsSeverityReview Article336S54S59Q2WOS:00036583460000926211653