McCune-Albright syndrome with fibrous dysplasia of the paranasal sinuses

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Tarih

1999

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Dergi ISSN

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Yayıncı

Erişim Hakkı

info:eu-repo/semantics/closedAccess

Özet

We report a 19-year old female patient with the McCune-Albright syndrome, which is a rare disease consisting of polyostotic fibrous dysplasia (FD) of bone associated with brown pigmented areas of the skin and several endocrine dysfunctions. The patient had FD involving the paranasal sinuses, the middle turbinate and the skull. The endocrine dysfunction of the patient concerns both growth hormone and prolactin hypersecretion. Because the patient had no major symptoms, neither surgical nor medical treatment was applied. Five-year follow-up revealed no complication and enlargement of the lesion.

Açıklama

Anahtar Kelimeler

Fibrous Dysplasia; Growth Hormone; Mccune-Albright Syndrome; Paranasal Sinuses; Skull, Growth Hormone; Prolactin; Adolescent; Albright Syndrome; Article; Cafe Au Lait Spot; Case Report; Edema; Epistaxis; Face Asymmetry; Facial Bone; Female; Fibrous Dysplasia; Growth Hormone Release; Headache; Human; Hyperprolactinemia; Hypertelorism; Hypertrophy; Nose Malformation; Nose Obstruction; Nose Septum; Paranasal Sinus; Telecanthus; Adolescent; Disease Progression; Female; Fibrous Dysplasia, Polyostotic; Follow-Up Studies; Humans; Paranasal Sinuses; Tomography, X-Ray Computed

Kaynak

Rhinology

WoS Q Değeri

Scopus Q Değeri

Q1

Cilt

37

Sayı

3

Künye